Moyamoya

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Abstract
MOYAMOYA desease (MMD) is a nonatherosclerotic, noninflammatory, nonamyloid vasculopathy characterized by chronic progressive stenosis or occlusion of the terminal internal carotid arteries and/or the proximal portion of the anterior cerebral arteries and/or middle cerebral arteries. The diagnosis of MMD is based on angiographic features. In 1957, the abnormal vessels at the base of the brain in MMD were first described as having a "hazy, cloudy puff of smoke" appearance, which led to the term moyamoya.1 The terms moyamoya disease and moyamoya syndrome are often used interchangeably, but most authors reserve the term moyamoya disease for the idiopathic form of this arteriopathy.