Comparative effects of lovastatin and chenodeoxycholic acid on plasma cholestanol levels and abnormal bile acid metabolism in cerebrotendinous xanthomatosis
- 1 July 1994
- journal article
- case report
- Published by Elsevier in Metabolism
- Vol. 43 (8) , 1018-1022
- https://doi.org/10.1016/0026-0495(94)90183-x
Abstract
No abstract availableKeywords
This publication has 22 references indexed in Scilit:
- Increased Concentrations of Cholestanol and Apolipoprotein B in the Cerebrospinal Fluid of Patients with Cerebrotendinous XanthomatosisNew England Journal of Medicine, 1987
- Biosynthesis of bile acids in cerebrotendinous xanthomatosis. Relationship of bile acid pool sizes and synthesis rates to hydroxylations at C-12, C-25, and C-26.Journal of Clinical Investigation, 1985
- A novel pathway for biosynthesis of cholestanol with 7 alpha-hydroxylated C27-steroids as intermediates, and its importance for the accumulation of cholestanol in cerebrotendinous xanthomatosis.Journal of Clinical Investigation, 1985
- Long-Term Treatment of Cerebrotendinous Xanthomatosis with Chenodeoxycholic AcidNew England Journal of Medicine, 1984
- Cerebrotendinous xanthomatosis: biochemical response to inhibition of cholesterol synthesis.BMJ, 1983
- Cerebrotendinous xanthomatosis: a defect in mitochondrial 26-hydroxylation required for normal biosynthesis of cholic acid.Journal of Clinical Investigation, 1980
- Cholic Acid BiosynthesisJournal of Clinical Investigation, 1979
- Chenodeoxycholic acid inhibits increased cholesterol and cholestanol synthesis in patients with cerebrotendinous XanthomatosisBiochemical Medicine, 1975
- A Biochemical Abnormality in Cerebrotendinous Xanthomatosis IMPAIRMENT OF BILE ACID BIOSYNTHESIS ASSOCIATED WITH INCOMPLETE DEGRADATION OF THE CHOLESTEROL SIDE CHAINJournal of Clinical Investigation, 1974
- The Metabolism of Cholestanol, Cholesterol, and Bile Acids in Cerebrotendinous XanthomatosisJournal of Clinical Investigation, 1973