C27 Bile Acids in Infants with Coprostanic Acidemia and Occurrence of a 3alpha,7alpha,12alpha-Trihydroxy-5beta-C29 Dicarboxylic Bile Acid as a Major Component in Their Serum
- 1 December 1979
- journal article
- research article
- Published by Wiley in European Journal of Biochemistry
- Vol. 102 (1) , 173-183
- https://doi.org/10.1111/j.1432-1033.1979.tb06278.x
Abstract
No abstract availableThis publication has 24 references indexed in Scilit:
- Defects of Bile Acid Synthesis in Zellweger's SyndromeScience, 1979
- A metabolic disorder similar to Zellweger syndrome with hepatic acatalasia and absence of peroxisomes, altered content and redox state of cytochromes, and infantile cirrhosis with hemosiderosisEuropean Journal of Nuclear Medicine and Molecular Imaging, 1977
- A 25-hydroxylation pathway of cholic acid biosynthesis in man and rat.Journal of Clinical Investigation, 1976
- The metabolism of 3alpha, 7alpha, 12alpha-trihydorxy-5beta-cholestan-26-oic acid in two siblings with cholestasis due to intrahepatic bile duct anomalies. An apparent inborn error of cholic acid synthesis.Journal of Clinical Investigation, 1975
- Hepatic ductular hypoplasia associated with characteristic facies, vertebral malformations, retarded physical, mental, and sexual development, and cardiac murmurThe Journal of Pediatrics, 1975
- Peroxisomal and Mitochondrial Defects in the Cerebro-Hepato-Renal SyndromeScience, 1973
- A novel fragmentation of trimethylsilyl ethers of 3β-hydroxy-Δ5-steroidsJournal of Mass Spectrometry, 1973
- Bice Salts of AnuraCHEMICAL & PHARMACEUTICAL BULLETIN, 1973
- Trihydroxycoprostanic acid in the duodenal fluid of two children with intrahepatic bile duct anomaliesBiochimica et Biophysica Acta (BBA) - General Subjects, 1972
- Metabolism of β-sitosterol in manJournal of Clinical Investigation, 1970