Macroglossia as a Presentation of the Beckwith-Wiedemann Syndrome
- 1 February 1985
- journal article
- case report
- Published by Wolters Kluwer Health in Plastic and Reconstructive Surgery
- Vol. 75 (2) , 170-176
- https://doi.org/10.1097/00006534-198502000-00004
Abstract
Plastic surgeons are not infrequently required to reduce the size of a large tongue in a child. Macroglossia is one of the main presenting features of the Beckwith-Wiedemann syndrome. This comprises a spectrum of disorders that includes a high incidence of malignancy. Patients with this syndrome should be identified and carefully assessed to exclude serious complications. This paper reports a series of 30 patients presenting to the Royal Children's Hospital over an 8-year period. An incidence of malignancy of 10 percent is recorded.Keywords
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