Abstract
A patient with multiple congenital anomalies suggestive of the "Cat eye" syndrome was found to have an extra marker bisatellited chromosome 22 derived from a maternal Y/22 translocation, identified by multiple banding patterns in cultures treated with DA. The proband''s karotype is 47,XX,+psu idic(22)(Yqter .fwdarw. Yq12::22p13 .fwdarw. 22q11::22q11 .fwdarw. 22p13::Yq12 .fwdarw. Yqter), t(22;Y)(p13;q12)mat., being tetrasomic for 22pter .fwdarw. q11, and trisomic for Yqh. Similarity between his clinical features and reported "Cat eye" cases, confirms that this region is responsible for the phenotypical expression of the syndrome.