THE CRITICAL SEGMENT FOR THE LANGER-GIEDION SYNDROME - 8Q24.11-]Q24.12

  • 1 January 1985
    • journal article
    • research article
    • Vol. 28  (4) , 224-227
Abstract
An 18-year-old intellectually normal male with characteristic features of the Langer-Giedion syndrome is reported. High resolution chromosome analysis showed a small deletion in the region of bands 8q24.11 and 8q24.12 in addition to an apparently balanced de novo translocation (21;9) (q2;q13). This finding provides additional information on the minimum deleted segment required to produce the Langer-Giedion syndrome and may indicate that deletions of this size or smaller are not necessarily associated with mental retardation.