Urethral Encirclement by Sacrococcygeal Teratoma

Abstract
Obstruction and neurogenic bladder involvement are common with sacrococcygeal teratomas but external genital involvement is rare. A genetic (46XY) male infant required cystotomy, colostomy and sex-of-rearing change to enable surgical removal of a sacrococcygeal teratoma that surrounded the hypospadiac urethra and deviated the penis. An associated ventral congenital transposition of the scrotum allowed partial coverage of the defect. Renal and bladder manifestations secondary to sacrococcygeal teratomas commonly require urologic management.