Hypoplasia of the optic nerve in an otherwise normal appearing eye is rare. A review of the literature revealed a total of 22 cases,1-3 half of which were unilateral. Recently, the value of optic foramen x-rays in establishing the diagnosis of unilateral hypoplasia of the optic nerve has been demonstrated.3,4 Report of a Case A 4-year-old Caucasian boy was referred because of esotropia and poor vision of the right eye. The esotropia had been present since birth. The child was the product of a normal pregnancy and delivery, and there was no other family history of eye disease. Except for the right esotropia, this child's growth and development had been normal. Vision was OD, light perception; OS, 20/30 (full line, "E"). Lids, lashes, and lacrimal apparatus were normal. The squint measured 14 prism diopters right esotropia (Krimsky), with full ductions. The right pupil reacted only consensually, and the