Reversible obstructive hypertrophic cardiomyopathy in the Beckwith-Wiedemann syndrome

1 September 1989

journal article
case report
Published by Springer Nature in Pediatric Cardiology

Vol. 10 (4) , 225-228
https://doi.org/10.1007/bf02083298

Abstract

Patients with the Beckwith-Wiedemann (B-W) syndrome have been reported to have an increased risk of congenital heart disease and of idiopathic cardiomegaly on chest x-ray. In the infant described here, reversible obstructive hypertrophic cardiomyopathy was documented and its relationship to the metabolic features of the B-W syndrome is discussed.

Keywords

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