Glycogenosis type IV: liver transplant at 12 years.
- 1 November 1994
- journal article
- case report
- Published by BMJ in Archives of Disease in Childhood
- Vol. 71 (5) , 450-451
- https://doi.org/10.1136/adc.71.5.450
Abstract
Hepatomegaly, the presenting feature of type IV glycogen storage disease at 20 months of age, regressed during childhood. The patient remained asymptomatic until 12 years of age when, after an episode of shock, septicaemia, and spontaneous peritonitis, liver transplantation was successfully performed.Keywords
This publication has 4 references indexed in Scilit:
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