Association of Atrioventricular Valve Atresia with Single Ventricle, Truncus Arteriosus Communis and Transposition

Abstract
A heart case [child] is presented showing a rare combination of atrioventricular valve atresia with single ventricle, truncus arteriosus communis with an anteriorly placed trunk (transposition). Because of the problems involved in the classification of this heart, the types of single ventricle are revised with particular attention to the rare cases of atrioventricular valve atresia and single ventricle reported in the literature. The rare type of truncus arteriosus communis with truncoatrioventricular valve discontinuity is excluded from the so-called transposition complexes, and properly classified as a form of truncus. The literal meaning of transposition is stressed and congenital heart defects should be approached in a purely anatomic sense with definition of each segment as accurately as possible.