d-Penicillamine in Wilson's disease presenting as acute liver failure with hemolysis
- 1 December 1982
- journal article
- case report
- Published by Springer Nature in Digestive Diseases and Sciences
- Vol. 27 (12) , 1126-1129
- https://doi.org/10.1007/bf01391452
Abstract
Wilson's disease in a young woman presenting with an acute course is described. The clinical manifestations were fulminant hepatic failure associated with marked intravascular hemolysis. Immediated-penicillamine and high-dose steroid therapy did not infuence the course of the disease. Necropsy revealed an increased hepatic copper content and cirrhosis with extensive necrosis of the liver.Keywords
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