Physiological significance of fatty acid elongation system in adrenoleukodystrophy
- 30 June 1991
- journal article
- Published by Elsevier in Journal of the Neurological Sciences
- Vol. 103 (2) , 188-194
- https://doi.org/10.1016/0022-510x(91)90163-2
Abstract
No abstract availableKeywords
This publication has 23 references indexed in Scilit:
- Topographical localization of peroxisomal acyl-CoA ligases: differential localization of palmitoyl-CoA and lignoceroyl-CoA ligasesBiochemistry, 1990
- Inhibitory effect of very-long-chain monounsaturated fatty-acyl-CoAs on the elongation of long-chain fatty acid in swine cerebral microsomesBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1988
- Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders.Journal of Clinical Investigation, 1987
- Lignoceroyl‐CoASH ligase: enzyme defect in fatty acid β‐oxidation system in X‐linked childhood adrenoleukodystrophyFEBS Letters, 1986
- The Cerebrohepatorenal (Zellweger) SyndromeNew England Journal of Medicine, 1984
- Abnormality of Long‐Chain Fatty Acids in Erythrocyte Membrane Sphingomyelin from Patients with AdrenoleukodystrophyJournal of Neurochemistry, 1981
- High concentration of hexacosanoate in cultured skin fibroblast lipids from adrenoleukodystrophy patientsBiochemical and Biophysical Research Communications, 1978
- Qualitative alteration in substrate specificity of mitochondrial monoamine oxidase in brainJournal of Neurochemistry, 1976
- Peroxisomal and Mitochondrial Defects in the Cerebro-Hepato-Renal SyndromeScience, 1973
- A RAPID METHOD OF TOTAL LIPID EXTRACTION AND PURIFICATIONCanadian Journal of Biochemistry and Physiology, 1959