Giant-Cell Fibroblastoma and Dermato Fibro Sarcoma Protuberans: The Same Tumoral Spectrum?
- 1 December 2000
- journal article
- case report
- Published by Georg Thieme Verlag KG in European Journal of Pediatric Surgery
- Vol. 10 (06) , 390-394
- https://doi.org/10.1055/s-2008-1072398
Abstract
We describe two cases of giant-cell fibroblastoma (GCF) with dermato fibro sarcoma protuberans (DFSP) component, occurring in two children in a chest wall localization. One case recurred 1 year later. The two patients were tumor-free 12 and 8 years later. GCF is a rare mesenchymal cutaneous and subcutaneous tumor reported mostly in the first two decades of life. Dermato fibro sarcoma protuberans, occurring preferentially in adults, is a rare skin tumor with a pronounced tendency to local recurrence. Some cases of association of recurrence of GFC under the form of DFSP have been reported, raising the question of a continuum between the two tumors. The treatment of choice of the two tumors is a wide local excision.Keywords
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