Pulmonary and Extrapulmonary Lymphangioleiomyomatosis Report of a Case with Bilateral Renal Angiomyolipomas, Multifocal Lymphangioleiomyomatosis, and a Glial Polyp of the Endocervix
- 1 September 1986
- journal article
- case report
- Published by Wolters Kluwer Health in The American Journal of Surgical Pathology
- Vol. 10 (9) , 650-657
- https://doi.org/10.1097/00000478-198609000-00007
Abstract
The authors report an extraordinary case of a 33-year-old female who had pulmonary and extrapulmonary lymphangioleiomyomatosis, bilateral renal angiomyolipomas, multifocal lymphangioleiomyomatosis involving the uterus, ovaries, periadrenal vessels, and liver. The patient also had a glial polyp of the endocervix which represented retained fetal parts from an abortion 15 years earlier. Both ovaries showed multiple follicle cysts which may have been a source of endogenous estrogen. The classical stigmata of the tuberous sclerosis complex were absent. The multifocal lymphangioleiomyomatosis of the various organs described presents an extremely rare manifestation of this disorder.Keywords
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