Primary rhabdomyosarcoma of the heart in an adult has not yet been reported in the literature. It is our purpose in this paper to report such a case and to discuss briefly primary tumors of the heart. The literature of this subject has been reviewed by Perlstein,1Goldstein,2Beck and Thatcher,3Nowicki4and Morris,5who gives comprehensive references to the literature of secondary growths in the heart. Goldstein in his opening paragraph states that "tumors of the heart are uncommon; primary growths are rare; primary sarcoma of the heart is a very rare finding." According to Perlstein the heart is the least frequent site of primary neoplastic change, while Adami6remarks that "the heart above all organs is constantly in a state of great efficiency, well nourished, well innervated and functionally always active, so that it is less likely to take on aberrant growth."