Incontinentia Pigmenti
- 1 August 1978
- journal article
- research article
- Published by American Medical Association (AMA) in Archives of Dermatology
- Vol. 114 (8) , 1182-1186
- https://doi.org/10.1001/archderm.1978.01640200036009
Abstract
• A child with incontinentia pigmenti (Bloch-Sultzberger syndrome) had recurrent pneumococcal meningitis and pneumococcal bacteremia with associated subdural hematomas. Immunologic evaluation revealed defective neutrophil chemotaxis with normal neutrophil chemiluminescense. In addition, lymphocytes showed a depressed proliferative response to phytohemagglutinin stimulation. An immunologic defect may prove to be part of this syndrome. (Arch Dermatol 114:1182-1186, 1978)This publication has 7 references indexed in Scilit:
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