A Case of CD3 +, CD4−, CD8−, WT31Acute T-Cell Leukemia

Abstract
The article reports a case of acute T-cell leukemia (T-ALL) with the unusual CD3+, WT31 phenotype. On surface marker analysis, the blast cells were found to be CD7+, CD2, CD5, CD1, CD4, CD8, CD3+ and negative for B-lymphoid and myeloid lineage. The cells had both TCRβ and TCRγ gene rearrangement but had negative results with the monoclonal antibody WT31, which reacts with a framework epitope on the Tα/β heterodimer (Ti) of the conventional T-cell receptor (TCR). This suggests an association of the CD3 molecular complex with a different polypeptide (the alternate TCRγ). In two similar reported cases of T-ALL (WT31, CD3+, CD4, CD8), the CD3 molecular complex was found to be associated with a product of the Tγ gene.

This publication has 0 references indexed in Scilit: