The rare case of a 62 years old male with functioning carcinoma of the exocrinic pancreas, liver metastases, and subcutaneous fat necrosis is described. Only 22 relating cases were found in the literature. Referring to published observations the symptomatology of these pancreatic tumours is analysed. The panniculitis which is part of the symptoms corresponds to the Weber-Christian disease or erythema nodosum. It is supposed that lipase-secreting carcinomas of the pancreas occur more frequently than hitherto believed.