Acute sensory neuronopathy with preserved SEPs and long‐latency reflexes

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Abstract
A case of spontaneous acute sensory neuronopathy is described in a previously healthy 19‐year‐old male. He had marked sensory ataxia with relative sparing of cutaneous sensation. There was no recovery over 4 years. Sural nerve biopsy showed modest axonal loss. Sensory evoked potentials were mildly abnormal in the face of absent sensory nerve action potentials. The long‐latency (R2) reflex was preserved whereas the short‐latency (R1) reflex was absent. The findings indicate that loss of large‐diameter (groupla) ganglion cells are primarily responsible for this syndrome.