Chronic recurrent demyelinating encephalomyelitis associated with hemophagocytic lymphohistiocytosis
- 1 January 1983
- journal article
- research article
- Published by Springer Nature in Acta Neuropathologica
- Vol. 59 (1) , 25-30
- https://doi.org/10.1007/bf00690313
Abstract
A man aged 31 with remittent fever, leukopenia, polyuria, and splenomegaly in addition to chronic and recurrent episodes of neurologic abnormalities was examined pathologically. A chronic type of perivenous encephalomyelitis was found in the CNS, and chronic inflammatory lesions were noticed in the infundibulo-hypophyseal system and also in the peripheral nerves. Moreover, hemophagocytic lymphohistiocytosis predominated in the reticuloendothelial system. This seemed to be the first adult case of demyelinating disease with hemophagocytic lymphohistiocytosis.Keywords
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