Cultured fibroblasts from patients with Niemann-Pick disease type C and type D exhibit distinct defects in cholesterol esterification
- 1 February 1992
- journal article
- Published by Elsevier in Biochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism
- Vol. 1124 (1) , 29-35
- https://doi.org/10.1016/0005-2760(92)90122-c
Abstract
No abstract availableKeywords
This publication has 26 references indexed in Scilit:
- Intracellular transport of cholesterol in type C Niemann-Pick fibroblastsBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1989
- The intracellular transport of low density lipoprotein-derived cholesterol is defective in Niemann-Pick type C fibroblasts.The Journal of cell biology, 1989
- Cycloheximide sensitivity in regulation of acyl coenzyme A:cholesterol acyltransferase activity in Chinese hamster ovary cells. 1. Effect of exogenous sterolsBiochemistry, 1986
- A Receptor-Mediated Pathway for Cholesterol HomeostasisScience, 1986
- The effects of low-density lipoprotein and cholesterol on acyl-coenzyme A: cholesterol acyltransferase activity in membranes from cultured human fibroblastsBiochemical Journal, 1983
- Esterification of cholesterol and 25-hydroxycholesterol by rat liver microsomesBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1983
- Dual modulation of hepatic and intestinal acyl‐CoA: cholesterol acyltransferase activity by (de‐)phosphorylation and substrate supply in vitroFEBS Letters, 1983
- [19] Receptor-mediated endocytosis of low-density lipoprotein in cultured cellsPublished by Elsevier ,1983
- Acyl-CoA:Cholesterol acyltransferase in chinese hamster ovary cellsBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1982
- The Low-Density Lipoprotein Pathway and its Relation to AtherosclerosisAnnual Review of Biochemistry, 1977