β-Galactosidase-deficient mouse as an animal model for GM1-gangliosidosis
- 1 January 1997
- journal article
- Published by Springer Nature in Glycoconjugate Journal
- Vol. 14 (6) , 729-736
- https://doi.org/10.1023/a:1018573518127
Abstract
GM1-gangliosidosis is a progressive neurological disease in humans caused by deficiency of lysosomal acid β-galactosidase, which hydrolyses the terminal β-galactosidic residue from ganglioside GM1...Keywords
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