Levels of mutant huntingtin influence the phenotypic severity of Huntington disease in YAC128 mouse models
- 1 February 2006
- journal article
- Published by Elsevier in Neurobiology of Disease
- Vol. 21 (2) , 444-455
- https://doi.org/10.1016/j.nbd.2005.08.007
Abstract
No abstract availableKeywords
This publication has 47 references indexed in Scilit:
- NMDA receptor function in mouse models of Huntington diseaseJournal of Neuroscience Research, 2001
- Transgenic mouse models of neurodegenerative disease caused by CAG/polyglutamine expansionsMolecular Medicine Today, 1997
- Aggregation of Huntingtin in Neuronal Intranuclear Inclusions and Dystrophic Neurites in BrainScience, 1997
- Formation of Neuronal Intranuclear Inclusions Underlies the Neurological Dysfunction in Mice Transgenic for the HD MutationCell, 1997
- Mouse Models of Human CAG Repeat DisordersBrain Pathology, 1997
- The relationship between trinucleotide (CAG) repeat length and clinical features of Huntington's diseaseNature Genetics, 1993
- Does impairment of energy metabolism result in excitotoxic neuronal death in neurodegenerative illnesses?Annals of Neurology, 1992
- Chronic quinolinic acid lesions in rats closely resemble Huntington's diseaseJournal of Neuroscience, 1991
- Excitotoxic injury of the neostriatum: a model for Huntington's diseaseTrends in Neurosciences, 1990
- Abnormalities of Striatal Projection Neurons andN-Methyl-D-Aspartate Receptors in Presymptomatic Huntington's DiseaseNew England Journal of Medicine, 1990