Lipoid Proteinosis (of Urbach-Wiethe)
- 1 February 1963
- journal article
- research article
- Published by American Medical Association (AMA) in Archives of Ophthalmology (1950)
- Vol. 69 (2) , 174-179
- https://doi.org/10.1001/archopht.1963.00960040180008
Abstract
Introduction Lipoid proteinosis is a rare disease of skin and mucous membranes. Characteristic lesions of the eyelid occur, but we have found only one case in the ophthalmic literature.1Although the earliest clinical report appeared in 1908, it was not until Urbach and Wiethe's 1929 article that the disease was extensively studied. Scattered reports have appeared since, mostly in the dermatologic and otolaryngologic literature. Various names have been given the disease. "Lipoidosis cutis et mucosae" was Urbach and Wiethe's 1929 term. Urbach renamed it "Lipoid proteinosis" in 1932 and Lundt in 1949 coined "Hyalinosis cutis et mucosae." McCusker and Caplan (1962) have suggested "Lipoglycoproteinosis." The characteristic lesions on mucous membranes and later on the skin, are small, translucent, yellowish papules. Less frequently they may appear as yellowish plaques. Hoarseness due to vocal cord involvement is the commonest complaint. Although not present at birth, lipoid proteinosis begins in infancy orKeywords
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