Corneodesmosomal Cadherins Are Preferential Targets of Stratum Corneum Trypsin- and Chymotrypsin-like Hyperactivity in Netherton Syndrome
- 1 July 2006
- journal article
- Published by Elsevier in Journal of Investigative Dermatology
- Vol. 126 (7) , 1622-1632
- https://doi.org/10.1038/sj.jid.5700284
Abstract
No abstract availableKeywords
This publication has 52 references indexed in Scilit:
- hK5 and hK7, two serine proteinases abundant in human skin, are inhibited by LEKTI domain 6British Journal of Dermatology, 2005
- Agonists of Proteinase-Activated Receptor-2 Stimulate Upregulation of Intercellular Cell Adhesion Molecule-1 in Primary Human Keratinocytes via Activation of NF-kappa BJournal of Investigative Dermatology, 2005
- Spink5-deficient mice mimic Netherton syndrome through degradation of desmoglein 1 by epidermal protease hyperactivityNature Genetics, 2004
- Degradation of Corneodesmosome Proteins by Two Serine Proteases of the Kallikrein Family, SCTE/KLK5/hK5 and SCCE/KLK7/hK7Journal of Investigative Dermatology, 2004
- LEKTI proteolytic processing in human primary keratinocytes, tissue distribution and defective expression in Netherton syndromeHuman Molecular Genetics, 2003
- PARticipation in inflammationJournal of Clinical Investigation, 2003
- Netherton Syndrome: Disease Expression and Spectrum of SPINK5 Mutations in 21 FamiliesJournal of Investigative Dermatology, 2002
- Mutations in SPINK5, encoding a serine protease inhibitor, cause Netherton syndromeNature Genetics, 2000
- Stratum Corneum Tryptic Enzyme in Normal Epidermis: a Missing Link in the Desquamation Process?11The authors declared in writing to have no conflict of interest.Journal of Investigative Dermatology, 2000
- Netherton’s Syndrome: A Severe Neonatal DiseaseDermatology, 1996