Oculopharyngeal muscular dystrophy: Potential therapies for an aggregate-associated disorder
- 1 January 2006
- journal article
- review article
- Published by Elsevier in The International Journal of Biochemistry & Cell Biology
- Vol. 38 (9) , 1457-1462
- https://doi.org/10.1016/j.biocel.2006.01.016
Abstract
No abstract availableKeywords
This publication has 28 references indexed in Scilit:
- Deleterious and protective properties of an aggregate-prone protein with a polyalanine expansionHuman Molecular Genetics, 2005
- An Essential Cytoplasmic Function for the Nuclear Poly(A) Binding Protein, PABP2, in Poly(A) Tail Length Control and Early Development in DrosophilaDevelopmental Cell, 2005
- Lithium rescues toxicity of aggregate-prone proteins in Drosophila by perturbing Wnt pathwayHuman Molecular Genetics, 2005
- The other trinucleotide repeat: polyalanine expansion disordersPublished by Elsevier ,2005
- Inclusion body formation reduces levels of mutant huntingtin and the risk of neuronal deathNature, 2004
- Inhibition of insulin amyloid formation by small stress moleculesFEBS Letters, 2004
- Oculopharyngeal muscular dystrophy-like nuclear inclusions are present in normal magnocellular neurosecretory neurons of the hypothalamusHuman Molecular Genetics, 2004
- Congo red, doxycycline, and HSP70 overexpression reduce aggregate formation and cell death in cell models of oculopharyngeal muscular dystrophyJournal of Medical Genetics, 2004
- Involvement of the ubiquitin-proteasome pathway and molecular chaperones in oculopharyngeal muscular dystrophyHuman Molecular Genetics, 2003
- Mammalian, Yeast, Bacterial, and Chemical Chaperones Reduce Aggregate Formation and Death in a Cell Model of Oculopharyngeal Muscular DystrophyJournal of Biological Chemistry, 2002