Abstract
A family in which hereditary nerve deafness occurred together with diabetes is reported. The inheritance pattern is dominant and the hearing loss is of a slowly progressing type with a sloping audiometric curve. The diabetes seems to make the hearing loss worse, but the genetical relation between the diabetes and the hereditary nerve deafness has not been established. There are also in the family other developmental anomalies, and the possibility that this might be part of a full syndrome is mentioned.