Mass spectrometric identification of abnormal aromatic compounds in the urine of a child with Reye's like syndrome

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Abstract
The urine of a young child with hypoglycemia and a Reye's like syndrome contained an excess of unusual aromatic products with a three carbon chain, phenylpropionylglycine and 3‐ and 4‐(hydroxyphenyl)propionic and 3‐(3‐methoxy‐4‐hydroxyphenyl)propionic acids, as well as of organic acids usually found in fatty acid β‐oxidation defects: the mono‐ and dicarboxylic acids derived from the respective (ω – 1) and ω‐oxidation of C6 to C10 fatty acids.