RETICULAR DYSGENESIS - REPORT OF 2 BROTHERS
- 1 January 1979
- journal article
- research article
- Vol. 38 (3) , 615-620
Abstract
Two brothers had marked leukopenia, lymphopenia, no immunological respnse to infections (no Ig [immunoglobulin] production, negative PHA [phytohemagglutinin] response and very low number of T [thymus-derived] and B [bone marrow-derived] lymphocytes in peripheral blood) and hypocellular marrow. They died at 12 and 8 days of life with infection of (Escherichia coli and Klebsiella, respectively).This publication has 11 references indexed in Scilit:
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