Dermatofibrosarcoma protuberans with lymph node and pulmonary metastases

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Abstract
Dermatofibrosarcoma protuberans is a locally aggressive histiocytic tumor that, on rare occasions, may metastasize to regional lymph nodes or distant sites. A dermatofibrosarcoma protuberans with lymph node involvement was reported in a 27 yr old woman. The tumor recurred repeatedly after local excisions, and 10 yr after the 1st resection, widespread pulmonary metastases developed in the patient and she died 4 yr later. More than 400 patients with dermatofibrosarcoma protuberans were reported in the literature. Including the present case, 5 patients had lymph node metastases, 17 patients had hematogenous spread and 3 had lymphatic and blood-borne metastases.