Anaesthesia for emergency ventriculo-peritoneal shunt in an adolescent with Noonan′s syndrome
Open Access
- 1 January 2014
- journal article
- case report
- Published by Medknow in Indian Journal of Anaesthesia
- Vol. 58 (4) , 452-5
- https://doi.org/10.4103/0019-5049.138991
Abstract
A 15-year-old boy with Noonan's syndrome was admitted for emergency ventriculo-peritoneal shunt. Intraoperative course was complicated by hypertensive urgency, which was effectively managed with high doses of esmolol (500 μg/kg/min). Difficult airway was anticipated due to presence of webbed neck and facial dysmorphism. Tracheal intubation was however successfully accomplished with the aid of a bougie. This report thus highlights the unique anaesthetic problems encountered during anaesthetic management of such a case, which is worth sharing.Keywords
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