X‐short arm deletion gonadal dysgenesis in two siblings due to unique translocation (Xp‐;16p+)

Abstract
A family demonstrating short arm deletion of the X chromosome as a consequence of X-16 balanced translocation in the mother is reported. The 2 Xp- sisters exhibit clinical signs of gonadal dysgenesis, while the balanced carriers are phenotypically normal. This represents the only example of both the balanced carrier state for an X translocation and its genetic consequence occurring in the offspring, as well as the involvement of X-16 interchange. Additional cases (37) of verified X translocations are discussed.