Kindler Syndrome in Native Americans From Panama

Abstract
In 1954, Theresa Kindler described progressive poikiloderma with marked diffuse cutaneous atrophy associated with congenital acral bullae and photosensitivity in a 14-year-old girl.1 She hypothesized that the syndrome might result from the coincidence in 1 patient of 2 rare congenital conditions (dystrophic epidermolysis bullosa and congenital poikiloderma) or might be due to a previously unidentified genetic disorder. Many subsequent reports have established this syndrome as a distinct clinical entity.2-11