Alimentary Tract Ganglioneuromatosis-Lipomatosis, Adrenal Myelolipomas, Pancreatic Telangiectasias, and Multinodular Thyroid Goiter: A Possible Neuroendocrine Syndrome
Open Access
- 1 June 1985
- journal article
- case report
- Published by Oxford University Press (OUP) in American Journal of Clinical Pathology
- Vol. 83 (6) , 744-747
- https://doi.org/10.1093/ajcp/83.6.744
Abstract
Diffuse, alimentary tract ganglioneuromatosis-lipomatosis, bilateral adrenal myelolipomas, pancreatic telangiectasias, and a multinodular thyroid goiter were found at autopsy in a 56-year-old, white male with a history of insulin-dependent diabetes, hypertension, peptic ulcer, and remote cerebral infarction. The degree of atherosclerosis, arterionephrosclerosis, and cardiac disease found at autopsy did not correlate with the patient’s history or his sudden death. The typical features of the multiple endocrine neoplasia syndrome, type II-B, were not identified. The findings in this patient may represent a variant of the multiple endocrine neoplasia complex, or a separate, previously unrecognized syndrome.Keywords
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