SHULMANS SYNDROME - FASCIITIS WITH EOSINOPHILIA, PSEUDOSCLERODERMA WITH EOSINOPHILIA

  • 1 January 1977
    • journal article
    • research article
    • Vol. 104  (10) , 616-621
Abstract
Two new cases of the Shulman''s syndrome were reported. The main signs are the acute painful onset after an unusual physical exertion, the development of fasciitis, and (or) myositis, and (or) scleroderma of limbs, the absence of Raynaud''s phenomenon, visceral involvement and constant eosinophilia and hypergammaglobulinemia. The prognosis is good with an improvement sometimes spontaneous or coincident with prednisone therapy. An association with Gougerot-Sjoegren''s syndrome, and a familial case of morphea was also observed. The prognosis in this case is mediocre: failure of corticotherapy and incomplete remission with cyclophosphamide.

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