Epilepsy in the Setting of Neurocutaneous Syndromes
- 1 August 1993
- Vol. 34 (S3) , S71-S78
- https://doi.org/10.1111/j.1528-1167.1993.tb06261.x
Abstract
The neurocutaneous syndromes are characterized by congenital dysplastic abnormalities involving the skin and nervous system. The commonest neurocutaneous syndromes manifesting epilepsy are tuberous sclerosis and the Sturge-Weber syndrome. Neurofibromatosis and other lesser-known entities, such as epidermal nevus syndrome, are also known to be accompanied by epilepsy. These syndromes are not related to one another. This article reviews what has been learned about the epileptic syndromes in these disorders.Keywords
This publication has 64 references indexed in Scilit:
- Topographic Comparative Study of Magnetic Resonance Imaging and Electroencephalography in 34 Children with Tuberous SclerosisEpilepsia, 1990
- EPILEPSY AND DISORDERS OF NEURONAL MIGRATIONThe Lancet, 1990
- Magnetic resonance imaging in relation to EEG epileptic foci in tuberous sclerosisBrain & Development, 1990
- Tuberous sclerosis: prevalence in the Grampian Region of ScotlandJournal of Intellectual Disability Research, 1989
- Clinical, cytogenetic, and pedigree findings in 18 cases of Aicardi syndromeAmerican Journal of Medical Genetics, 1989
- Regional cerebral blood flow characteristics of the Sturge-Weber syndromePediatric Neurology, 1985
- Organoid Nevus Syndrome (Linear Nevus Sebaceus of Jadassohn): Clinical and Radiological Study of a CaseNeuropediatrics, 1977
- INFANTILE SPASMS AND SUBSEQUENT APPEARANCE OF TUBEROUS SCLEROSIS SYNDROMEThe Lancet, 1975
- "Incontinentia pigmenti achromians (Ito)"Archives of Dermatology, 1967
- On Epilepsy in Sturge‐Weber's DiseaseActa Psychiatrica Scandinavica, 1949