Hepatolenticular Degeneration (Wilson's Disease)

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Abstract
WILSON'S disease has for a long time been of particular interest to the neurologist because it exemplifies a specific metabolic disorder involving some special relation between hepatic cirrhosis and degeneration of the brain. The special fea tures of this relation have become of greater interest in recent years in the light of increasing knowledge of brain damage in hepatic coma and hepatic encephalopathy, in association with more common types of hepatic cirrhosis.Two different syndromes were originally described, those of pseudosclerosis described by Westphal1 in 1883 and the juvenile form, called "progressive lenticular degeneration" by Wilson2 in 1913. Since the . . .