FAMILIAL PAROXYSMAL DYSTONIA

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Abstract
"Paroxysmal dystonia," an uncommon disorder, is characterized by the assumption of unilateral dystonic postures without clonic movements or alteration of consciousness. These paroxysms may occur sporadically or in the course of multiple sclerosis, neuromyelitis optica, encephalitis lethargica, hepatolenticular degeneration and hypocalcemic tetany. This report presents the cases of 4 affected members of a family. In these cases, the pattern of inheritance is compatible with an autosomal dominant gene. The neuropathologic lesion is as yet undefined.