CARDIAC HAEMANGIO‐ENDOTHELIOSARCOMA Review of the Literature and Report of a Case

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Abstract
A case of primary hemangioendotheliosarcoma of the right atrium is reported. A review of the literature is given and in all but 4 of the 56 cases, the tumor originated in the right atrium projecting into the cavity. This explains why these tumors present a rather uniform clinical picture characterized by superior vena caval syndrome combined with pericardial effusion, cardiomegaly, dyspnea and chest pain. A male dominent sex distribution of 3:1 is found. The tumor is highly malignant and has caused death within an average of 6 mo. The possibility of early diagnosis was emphasized, particularly since the clinical symptoms are rather typical and cases are reported where therapy apparently was successful.

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