Mortality in Ehlers–Danlos Syndrome Due to Spontaneous Rupture of Large Arteries
- 17 December 1964
- journal article
- Published by Massachusetts Medical Society in New England Journal of Medicine
- Vol. 271 (25) , 1309-1310
- https://doi.org/10.1056/nejm196412172712508
Abstract
DISSECTING aneurysm of the aorta, although more commonly associated with Marian's syndrome, has been reported in several patients with Ehlers–Danlos syndrome.1 This complication has occurred in young persons and is presumably related to the generalized abnormality of connective tissue in this condition.The present report describes 2 boys with the syndrome who died after spontaneous rupture of large arteries — a popliteal artery in 1 and a subclavian artery in the other.Case ReportsCase 1. E.K., a 12-year-old boy, was renowned locally for the many lacerations and dislocations that he suffered as a result of ordinary trauma. He presented . . .Keywords
This publication has 4 references indexed in Scilit:
- Ehlers-Danlos syndrome with a sinus of valsalva aneurysm and aortic insufficiency simulating rheumatic heart diseaseThe American Journal of Medicine, 1963
- Repair of Cardiac Defect in Patient with Ehlers--Danlos Syndrome and Deficiency of Hageman FactorBMJ, 1961
- The Structure of the Connective Tissue, an Explanation of the Symptoms of the Ehlers-Danlos SyndromeDermatology, 1955
- EHLERS-DANLOS SYNDROME ASSOCIATED WITH THE TETRALOGY OF FALLOTArchives of Dermatology, 1950