Intravenous γ-Globulin Therapy in Diamond-Blackfan Anemia
- 1 April 1992
- journal article
- case report
- Published by Wiley in Pediatrics International
- Vol. 34 (2) , 179-180
- https://doi.org/10.1111/j.1442-200x.1992.tb00947.x
Abstract
Pure red cell aplasia (PRCA) is a rare disorder of erythrocyte production which is believed to have an autoimmune basis in most cases. Diamond-Blackfan anemia (DBA) is one type of congenital PRCA. Since PRCA has been reported to respond to intravenous gamma-globulin (IVGG) therapy, we administered IVGG to a 2 year old girl with DBA resistant to corticosteroids and observed slight therapeutic effect.Keywords
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