Papillon‐Lefévre Syndrome
- 1 January 1988
- journal article
- Published by Wiley in International Journal of Dermatology
- Vol. 27 (1) , 63-66
- https://doi.org/10.1111/j.1365-4362.1988.tb02344.x
Abstract
Papillon-Lefèvre syndrome is a rare autosomal recessive disorder of palmoplantar keratinization in which there is a unique association of the palmoplantar hyperkeratosis and premature loss of both deciduous and permanent teeth. We report three patients with papillon-lefèvre syndrome who showed a remarkable degree of improvement after treatment with an oral retinoid.Keywords
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