Model SV40-transformed fibroblast lines for metabolic studies of human prosaposin and acid ceramidase deficiencies
- 1 June 1997
- journal article
- Published by Elsevier in Clinica Chimica Acta; International Journal of Clinical Chemistry
- Vol. 262 (1-2) , 61-76
- https://doi.org/10.1016/s0009-8981(97)06527-3
Abstract
No abstract availableKeywords
This publication has 28 references indexed in Scilit:
- The serial cultivation of human diploid cell strainsPublished by Elsevier ,2004
- Targeted disruption of the mouse sphingolipid activator protein gene: a complex phenotype, including severe leukodystrophy and wide-spread storage of multiple sphingolipidsHuman Molecular Genetics, 1996
- Neurodegenerative course in ceramidase deficiency (Farber disease) correlates with the residual lysosomal ceramide turnover in cultured living patient cellsJournal of the Neurological Sciences, 1995
- Identification of the neurotrophic factor sequence of prosaposinThe FASEB Journal, 1995
- Stimulation of Acid Ceramidase Activity by Saposin DArchives of Biochemistry and Biophysics, 1994
- Sphingolipid Activator Protein D (sap-D) Stimulates the Lysosomal Degradation of Ceramide in VivoBiochemical and Biophysical Research Communications, 1994
- Activator proteins and topology of lysosomal sphingolipid catabolismBiochimica et Biophysica Acta (BBA) - Lipids and Lipid Metabolism, 1992
- Saposin proteins: structure, function, and role in human lysosomal storage disordersThe FASEB Journal, 1991
- Sphingolipid activator protein deficiency in a 16-week-old atypical Gaucher disease patient and his fetal sibling: Biochemical signs of combined sphingolipidosesEuropean Journal of Pediatrics, 1989
- Saposin D: A sphingomyelinase activatorBiochemical and Biophysical Research Communications, 1988