Long-term l-carnitine treatment in isovaleric acidemia
- 1 March 1991
- journal article
- case report
- Published by Elsevier in Pediatric Neurology
- Vol. 7 (2) , 137-140
- https://doi.org/10.1016/0887-8994(91)90011-9
Abstract
No abstract availableKeywords
This publication has 11 references indexed in Scilit:
- The Treatment of Isovaleric Acidemia with Glycine SupplementPediatric Research, 1988
- The response to l-carnitine and glycine therapy in isovaleric acidaemiaEuropean Journal of Pediatrics, 1986
- Urinary Excretion of l-Carnitine and Acylcarnitines by Patients with Disorders of Organic Acid Metabolism: Evidence for Secondary Insufficiency of l-CarnitinePediatric Research, 1984
- L-carnitine therapy in isovaleric acidemia.Journal of Clinical Investigation, 1984
- L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.Journal of Clinical Investigation, 1984
- Propionylcarnitine excretion in propionic and methylmalonic acidurias: a cause of carnitine deficiencyClinica Chimica Acta; International Journal of Clinical Chemistry, 1984
- Secondary carnitine insufficiency in disorders of organic acid metabolism: modulation of acyl-CoA/CoA ratios by l-carnitine in vivoBiochemical Society Transactions, 1983
- Glycine therapy in isovaleric acidemiaThe Journal of Pediatrics, 1978
- Carnitine metabolism in the fasting rat.Journal of Biological Chemistry, 1978
- Isovaleric AcidemiaNew England Journal of Medicine, 1967