Scarring is a characteristic symptom of pemphigus conjunctivae. In contrast, scarring does not occur in pemphigus vulgaris, pemphigus foliaceus or pemphigus vegetans, except following secondary infection of the lesions. The scarring in pemphigus conjunctivae is usually restricted to the mucous membranes, occurring regularly on the conjunctivas and occasionally on the mucous membranes of the mouth, nose, throat, esophagus, vulva and penis. The cutaneous lesions of pemphigus conjunctivae heal, as a rule, without scar formation. Only 5 instances of scarring of the skin were found in the literature. Recently 3 cases of pemphigus conjunctivae with scarring of the skin as well as of the mucous membranes have been observed at the Massachusetts General Hospital. Because of the rarity of scarring of the skin with this disease, it was felt that these 3 cases were worthy of publication. REVIEW OF THE LITERATURE The first case of pemphigus conjunctivae associated with cutaneous scarring