Corrected Transposition of the Great Arteries

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Abstract
Corrected transposition of the great arteries without associated intracardiac anomalies is a very rare condition.1 This lesion is also known as ventricular inversion with l-transposition. As with complete or d-transposition, the aorta arises from the right ventricle and the pulmonary artery from the left ventricle ( Figure 1 ), but in corrected transposition of the great arteries there is also ventricular inversion, so that the “right ventricle” is on the left side of the heart and is connected to the left atrium. Thus, pulmonary venous return to the left atrium flows to the morphologic right ventricle and is then ejected into the aorta. Systemic venous return to the right atrium flows to the morphologic left ventricle and is ejected into the pulmonary artery. Patients with corrected transposition of the great arteries are pink and asymptomatic and may survive with their conditions undiagnosed until adulthood. The majority of patients (90 percent) have a ventricular septal defect or pulmonary stenosis (80 percent) (or both),2 which often produces congestive heart failure due to incompetence of the left atrioventricular valve or gradual deterioration of the anatomic right ventricle. Complete heart block is also a common cause of death.3