Current concepts of respiratory complications of neuromuscular disease in children
- 1 June 2000
- journal article
- review article
- Published by Wolters Kluwer Health in Current Opinion in Pediatrics
- Vol. 12 (3) , 203-207
- https://doi.org/10.1097/00008480-200006000-00004
Abstract
Chronic neuromuscular diseases affect the respiratory muscles in varying patterns and degrees. As a result, patients with these disorders develop restrictive pulmonary disease, ineffective cough, atelectasis and pneumonia, and chronic respiratory insufficiency leading to respiratory failure. Therapeutic strategies are evolving to augment cough and airway clearance, improve lung volumes, and support the patient with progressive ventilatory failure. These techniques have improved longevity and quality of life for many patients with neuromuscular disease.Keywords
This publication has 19 references indexed in Scilit:
- Topical Review: Management of the Respiratory Complications of Neuromuscular Diseases in the Pediatric Intensive Care UnitJournal of Child Neurology, 1999
- Sniff Nasal Inspiratory PressureAmerican Journal of Respiratory and Critical Care Medicine, 1999
- Diaphragm thickness and inspiratory strength in patients with Duchenne muscular dystrophyThorax, 1997
- Clinical implications of maximal respiratory pressure determinations for individuals with duchenne muscular dystrophyArchives of Physical Medicine and Rehabilitation, 1997
- Chest wall compliance in infants and children with neuromuscular disease.American Journal of Respiratory and Critical Care Medicine, 1996
- Thoracoabdominal Pattern of Breathing in Neuromuscular DisordersChest, 1996
- Spinal Fusion in Duchenne's Muscular DystrophyJournal of Pediatric Orthopaedics, 1996
- Recruitment of some respiratory muscles during three maximal inspiratory manoeuvres.Thorax, 1993
- Respiratory Muscle Function in Myasthenia GravisAmerican Review of Respiratory Disease, 1988
- Atelectasis and Neuromuscular Respiratory FailureChest, 1984