Aortic Arch Syndrome with Special Reference to Pulseless Disease and Its Variants

Publisher Website
Google Scholar
Abstract
Thirteen of 14 cases of aortic arch syndrome experienced during the last 11 years were diagnosed as pulseless disease described by Shimizu and Sano, reflecting the high frequency of this disease in Japan. Six cases of atypical coarctation of the aorta seen during the same period of time were also analysed. The pathogenesis of atypical coarctation and pulseless disease were identical, based on the comparison of sex and age distribution, laboratory data and autopsy findings. It was recommended that these apparently different conditions be categorized under a single term, for example panaortitis syndrome, with subtypes such as aortic arch type, abdominal aorta type and extensive type according to the localization of the lesions. The prognosis of these patients seemed favorable despite the persistence of disability of varying degrees.

This publication has 3 references indexed in Scilit: