Rosai-Dorfman disease presenting with multiple orbital and intracranial masses
- 12 April 1996
- journal article
- case report
- Published by Springer Nature in Acta Neuropathologica
- Vol. 91 (5) , 554-557
- https://doi.org/10.1007/s004010050466
Abstract
Rosai-Dorfman disease is an idiopathic histocytic proliferative disorder typically characterized by painless cervical adenopathy, fever, and weight loss. Extranodal manifestations are responsible for presentation in approximately 25% of patients. Orbital involvement has been described in about 10% of patients. There have been only 16 reported cases of Rosai-Dorfman disease presenting with an intracranial mass. We report an unusual case of a patient presenting with bilateral orbital tumors as well as multiple intracranial masses. Clinical, magnetic resonance imaging, and histopathological features are discussed.Keywords
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